In human anatomy, an azygos lobe is a rare congenital variation of the upper lobe of the right lung. Embryologically, it arises from an anomalous lateral course of the azygos vein [1] [2] in a pleural septum within the upper lobe. As it has no bronchi, veins and arteries of its own, it is not a true, or even accessory, pulmonary lobe, but rather an anatomically separated part of the upper lobe. It is usually an incidental finding on chest x-ray or computed tomography and is as such not associated with any morbidity but can cause technical problems in thoracoscopic procedures [3].